Limited Cutaneous Scleroderma-Related Pulmonary Arterial Hypertension — a Case Report

severe acro-osteolysis in a case of limited cutaneous scleroderma

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The Relationship between Serum Pro‐Brain Natriuretic Peptide (Pro‐BNP) Levels and Pulmonary Arterial Hypertension (PAH) in Patients with Limited Scleroderma

Introduction: Pulmonary arterial hypertension (PAH) is a late progressive sclerodermarelated complication, which can lead to right heart failure and cor pulmonale. Given that cardiac catheterization is a diagnostic method of choice for PAH, and considering the high risks of this method, the purpose of this study was to evaluate the relationship between serum Pro‐Brain natriuretic peptide (Pro‐B...

Different right ventricular contractility in limited cutaneous systemic sclerosis- associated pulmonary arterial hypertension and idiopathic pulmonary arterial hypertension

Severe Acro-osteolysis in a Case of Limited Cutaneous Scleroderma

Systemic sclerosis (scleroderma) is a rare fetal autoimmune disease of connective tissue leading to skin fibrosis as well as internal organ involvement (1). An annual incidence rate of 2-20 and prevalence rate of 100-300 per million population have been estimated for scleroderma with a mean survival of 12 yr from diagnosis (2-4). Moreover, there is a considerable preponderance of female gender ...

Pulmonary Hypertension in a Patient with Non-cirrhotic Portal Hypertension and Scleroderma Sine Scleroderma: A Case Report

Porto-pulmonary hypertension is a known complication of liver cirrhosis but its association with noncirrhotic portal hypertension patients is rare. We report a case of pulmonary hypertension in a patient with noncirrhotic portal hypertension and scleroderma sine scleroderma. The two latter conditions have been shown to be independently associated with pulmonary arterial hypertension. DLCO is ex...